AORTIC SURGERY IN A PATIENT WITH MARFAN SYNDROME AND PECTUS EXCAVATUM

Abstract

Severe cardiovascular disorders, including aortic dissection and aneurismal dilation of the aorta, are the main life-threatening complications of the Marfan syndrome 1. Approximately two thirds of individuals who have this syndrome have chest wall deformities such as pectus excavatum or pectus carinatum 2. When a patient with pectus excavatum needs aortic surgery, the surgeon may face a major clinical challenge in choosing the optimal surgical approach 3. We present a case of the Marfan syndrome with severe pectus excavatum who underwent aortic surgery.